Zvinokonzera mafungiro ephis

Muchikamu chinoti "Zvinokonzera mavambo emakumbo epi" iwe uchawana ruzivo rwakakosha iwe pachako. Iropi ma cysts ane mitsetse yakazara mumvura mukati memafungiro epvo. Tsanga dzinogona kuve dzakabatana uye dzinowanikwa. Itsvo dzehitsvo dzakajairika.

Zvinorehwa nehutano hwepfungwa dzepisto hunotsanangurwa nezvimwe zvinotevera:

• Iropi ma cysts akajairika uye dzimwe nguva vanomirira basa rakaoma rekuongororwa kune vanachiremba-vanachiremba, vanachiremba, vanachirologist uye vane pathologist.

• Mamwe mafomu, akadai sepurocystic kidyo chirwere muvanhu vakuru, ndicho chikonzero chikuru chekubatanidza murwere mune chirongwa chehemodialysis.

• Zvigaro zvinogona kuguma zvikava zvironda zvinotyisa zvakaoma kuziva.

Simple cysts

Zvinyorwa zvisinganzwisisiki ndezvisina kuroorwa kana kuti zvakasiyana-siyana zvemasikirwo akasiyana-siyana, kubva pa1 kusvika ku10 masendimita. Tsanga dzinowanzokomberedza nekwenyoro yakajeka grey shell uye izere nemvura yakachena. Mutsvo, ma cysts anowanzotora nzvimbo yechipfuva (munharaunda ye cortex), kunyange zvazvo dzimwe nguva inogona kunge iri munharaunda (mukati medulla). Tsanga dziri muitsvo, sekutonga, hazvikonzeri zviratidzo uye zvakajairika kune vanhu vakwegura kupfuura makore makumi mashanu. Nekukura kukuru kwe cysts, marwadzo munharaunda yechipamende inogona kuitika, asi majeeti akadaro anowanzoonekwa aine njodzi paanoongorora itsvo dzeimwe hutano. Mhosva yekuparara kwemvura mumakristi anorondedzerwa, izvo murwere anonzwa sekunzwa kunorwadza kamwe kamwe munharaunda uye lumbar region. Kusveta kunogona kuva mutungamiriri wehuipi hwakaipa hwe cyst shell. Ne congenital multicystosis yeinso, mwana anoberekwa aine kuwedzera kwakanyanya kusinga kushanda kwetsvo, iyo iyo yakashandurwa ikava yakawanda ye cysts. Nekuparara kwenhengo dzemawere, fetus iri muUtero haigoni kubereka urini, zvichiita kuti zvinyanyisa amniotic fluid. Izvi zvinokonzera kukanganiswa kwe fetus nekuda kwekuwedzera kwechibereko chechibereko. Chiso chechibereko chakadaro chakasvibiswa, mhino inoputika, nzeve dziri pasi, uye mapapiro akadzika pasi pemaziso.

Kidney Removal

Varwere vane mafungiro emakumbo akawanda vanokurudzirwa nephrectomy - kubudiswa kwepfungwa. Kuvhiya kunoitwa kana kuwedzera kana kutapukirwa kwe-cysts, uyewo nehuwandu hwemhepo muurwere.

Polycystic inogadzirisa mamiriro ezvinhu. Kune marudzi mazhinji ehutachiwana:

• kubata pamuviri - mwana anoberekwa ane mafyvo makuru uye anofa nguva pfupi mushure mekuberekwa;

• vana vasina kuberekwa - vanoonekwa kuti mumwedzi wokutanga weupenyu;

• Vana - muvana vane makore 3 kusvika ku12, pane gaka rekukura uye kusagadzikana kwepvo. Zvimwe zviratidzo zvinosanganisira kukwira kweropa, kuwedzera kwechiropa uye spleen;

• vechidiki - chirwere chinowanikwa mukati memakore ekutanga ehupenyu;

• Mukuru - iyi mamiriro ezvinhu anowanikwa kune vanhu vakuru vanotakura zvezvinyorwa zvinotakura zvizere. Izvi zvinoreva kuti mumwe munhu anorwara akawana nhaka yechirwere chegene kubva kune mumwe wevabereki.

Chimwe chinokanganisa chiremera chemajini muchirwere chepurocystic muvanhu vakuru ndechekuchinja mutumbi wechromosome wechi16, iyo inokonzera kugadzirwa kwe polycystin protein. Iyo yekupedzisira inoita basa rinokosha mukubatana kwe intercellular. Zviratidzo zvepurocystic inetso dzinosanganisira kuputika, kurwadziwa munharaunda ye lumbar, hematuria (ropa mumuguta) uye kuwedzera kweropa. Kuora kweiyo kunogona kuonekwa nenzira yechirwere kana nekuda kwekuongororwa kwehama dzevarwere.

Diagnostics

Muvarwere vazhinji, chirwere ichi chinoonekwa pazera remakore makumi matatu nemakumi mashanu. Kura kwechimiro chekudzivirira kunowanikwa mune anenge chetatu chevarwere uye kunotungamirira kudikanwa ye dialysis, uyezve - kuchinja kwepvo.

Zvinogadzirisa zviratidzo

Polycystic inogona kugoverwa nedzimwe zviratidzo zvechirwere, zvinosanganisira, kunyanya:

• kuwedzera kwehutano (high blood pressure);

• Kuvharirwa kwechirwere chetsotsi;

• aneurysms (kukura kwemasvingo) eropi uye mamwe mishonga;

• Hernias uye diverticula yemukumbo.

Kurapa

Varwere vane chirwere cheal dialysis kana mushure mokunge vafemerwa vangave vachida kubvisa itsvo dzinoramba dzichiwedzera kuitira kudzivirira kubuda ropa, utachiona uye kurwadziwa.

Zvimwe zvirwere zvepfungwa zvepfungwa zvinosanganisira:

• Fanconi syndrome haisi chinhu chinowanikwa, yakagadzirirwa sechinhu chakakurumbira che X. Inozivikanwa neanemia, kushaya kweutsvo uye pasi yakanyanya muropa.

• Tsvete yepinyi - kuwedzera kwakakosha kwekutora tubhu. Chikamu chiduku, zvizere kana zvese zviviri zvinogona kuchinjwa. Izvi zvinowanzobatana nemamiriro ezvinhu anowanzobatanidzwa nehutu hweWilms (chirwere chinorwadza chepfungwa mukati mevana), aniridia (kusabatwa kwechiso cheziso) uye hemyhypertrophy (hypertrophy yemisungo yehafu yemuviri). Chirwere ichi chinowanzofambidzana nehutachiona hwehutachiona hwehutachiona, marombo ekugadzirwa uye mafungiro asina kukwana.

• Chirwere cheHippel-Lindau chirwere chemhuri chakakomba nekuvandudzwa kwemakumbo emakumbo e-cerebellum, retina, musana wemvura, dzimwe nguva pancreas uye adrenal gland mumamiriro ezvinhu e cystic yenyango kukuvara, izvo zvinowedzera kuipa.

• Zvirwere zvinosuruvarisa zveitsvo ndeyekuguma kwekuparadzwa kwechikamu chepakati chechirwere chekenza nekuumbwa kwekrisiti kana, zvakare, kuipa kwebenign cyst.