Congenital short epopus in children

Icho chinonyanya kukosha kwechirwere ichi chesophagus chiri muhutano hwemukati. Kungofanana nechirwere chinopisa, sopu iri panze ine ruvara rwakawanda, asi chikamu chacho kubva mukati chinowanikwa nechirwere epithelium. Nokudaro, chikamu chekuparara chepopu inonzi morphologically kuenderera kwemudumbu, uye sopu, naizvozvo, inopfupiswa.


Mukufamba kwemakore mazhinji, pakanga pasina kubvumirana mune mabhuku pamusoro penheyo yenguva shoma yenguva yakareba sekuzvimiririra kusimbiswa kwekunetseka. Mupiro mukuru kuna etiology, pathogenesis, kliniki-morphological data, kuongororwa uye kurapwa kwekuzvarwa kwepamukira kwenguva shoma kwakaitwa naB.Bretret (1959). Ichi chirwere chinotsanangurwa mumabhuku ari pasi pemazita akasiyana-siyana: brachiozophagus, chibereko chemuviri, kusagamuchirwa kwemudumbu, chikamu chepamuviri mudumbu.

Chimiro chekusimudzirwa kwechifupi chinotsanangurwa nekuputsa kwekugadzirwa kwechigamba chekudya mukati mokutanga kwemakryonic, apo sopu yakanga yakazara ne-cylindrical epithelium. Kubviswa kwe epithelium iyi, kutanga nechepakati chetatu chesophagus, kunovhiringidzika, semugumisiro wekuti chikamu chetatu chayo chakabatanidzwa nekamupa epithelium. Nokudaro pane dystopia ye gastric mucosa muchitsiko chepasi chesophagus (ine nzvimbo inowanzoitirwa cardia).

Kutendwa kwekufungidzira uku ndeyekuti chikamu che-supra-diaphragmatic chechinzi chisingatauri mudumbu, kunze kwemukati membrane, inoumbwa sechitubu uye isina chekuvhara serous. Muchikamu chimwechete, zvikamu zvemuviri uye zvenguva refu, maitiro ehutachiona, zvakasiyana, uye ropa rinowanikwa, sezvinowanzoitwa, kubva kune aorta.

Zviratidzo zvechipatara

Iko kusanganisa kwakasangana kwakasununguka kunofambidzana, sekutonga, ne gastroesophageal reflux, iyo yakaoma neesophagitis uye kutanga kwe peptic esophageal stenosis.

Iko kusanganisa kwakanyanya kwemavhenekeri kunoratidzwa kuvana vemakore matatu ekutanga ehupenyu, nokuti vane dare rakasimba re reflux syndrome. Mune anamnesis, varwere vakadaro vanowanzorutsira kakawanda mushure mekuberekwa. Kazhinji pane zviratidzo zvezvirwere zvinopfurikidza zvekufema: bronchitis, pneumonia (mumakumi matatu ematambudziko). Mune ramangwana, zvipatara zvinoratidzika zvichienderana nekuumbwa kwechipiri chepensten. Kana iyo stenosis isingaumbwa, chiratidzo chakanyanya kurutsa nekugadzirisa zviri mukati. Kusvetuka kunokonzerwa nokuchema, nechinzvimbo chakakosha chemuviri, uye nehutano hushoma hwenyama hunokonzera kuwedzera kwemuviri wepamuviri.Mvura yakaruka inowanikwa mumarutsi; nguva shoma kurutsa coffee. Nekudzivirira kwechipiri cheputi nemhaka yepptic ulcerative anopharyngitis, zviratidzo zvekuputsika kwekuvhara kwemajoka zvinowanzoita: dysphagia, kurutsa kwezvokudya.

Vana vakwegura kudarika makore masere vanonyunyutira kurwadziwa mushure me sternum, iyo inowanikwa iyo inokonzerwa neodisagia uye ulcerative esophagitis. Kazhinji, vana vanoedza kunwa pishchuk. Pamusana pekubuda ropa nguva dzose kubva muDystopic mucous membrane, sezvinopupurirwa nekusanganiswa kweropa mumarutsi emarutsi uye maitiro akanaka kune ropa rinenge risina kupera mumucheka, anemia inokura. Anemic syndrome inoonekwa mu 1/3 yevarwere. Vana vane hutano husina simba hwekuzvarwa hunochera shure kwekugadzirwa kwemuviri.

Kuti uwane hutano hwekuzvarwa kwenguva shoma, chirongwa che X-ray chinoshandiswa, nerubatsiro rwokuti, kutanga kwezvose, gastric reflux inowanikwa. MuTellelenburg nzvimbo, murwere we esophageal esophageal reflux akatsunga kukanda zvinhu zvakasiyana-siyana zveyvary mukati mehutu. Chikamu chekutarisa chegumbo, sekutonga, chakawedzerwa pasi zvichienderana nemafungiro kana bhero. Mifananidzo ye-X-ray munzvimbo yakasiyana-siyana inoratidza kubata kwenguva refu, inofananidzwa nemuchengetedze wemudumbu. Nharaunda yechipupuriro panguva yekuongororwa kwemurwere pakamira zvakamira. Nechirwere chechipiri, kushandiswa kwechimiro chakasiyana-siyana hachina kugadziriswa, uye kudzvinyirira kweiyo inogadziriswa pamusoro pekumanikidzwa.

Inowanzoshandiswa kushandiswa kweesophagofibroscopy. Chiratidzo chinonyanya kukosha endoscopic ndechekuchinja kwepamusoro kwemukatial lining of the poop in the gastric mucosa, i.ะต. pamusoro pekufungidzirwa kwechidimbu chinoputika. Mukusavapo kwe stenosis mumharapara, catarrhal kana ulcerative fibrinous esophagitis inowanikwa. Nekubudirira kwe stenosis, sekutonga, iri pamuganhu we mucous membrane yemudumbu uye sopu.

Maererano nechochokuti muvarwere vane chirwere chenguva shoma chine nguva inogara ine gastroesophageal reflux, chimwe chikonzero chekuongorora chinonzi ine intraepithelial pH-metry.

Vagari nechecheche vanoita zvakasiyana-siyana nekuongorora pamwe ne pyloric stenosis, pilorospasm, kucheneswa kwehutachiona hwechirafu, chalasia, congenital uye yakagadziriswa stenoses yeropa reparal.

Kurapa

Mushonga unowanzoshandiswa, unotarisirwa kubvisa gastroesophageal reflux.Kuvhiyiwa kwakanyanya kwechokwadi kunoshandiswa kweNN Kanshin mukugadziridzwa kweYF Isakova et al., Kubva pane gastroplication yemagetsi. Mamiriro ezvinhu apo kuberekwa kwenguva pfupi kunowanzoomeswa nepeptic stenosis , chirwere chinonzi antireflux chinowedzerwa nekuiswa kwegastrostomy. Mune ramangwana, yakasimbiswa nemagetsi.

Kubva pakuona kwevakiriniki vachifunga kuti chirwere chepachidiki chinokonzerwa nekusavhiringidza mudumbu, zvinokosha kuitisa chirwere chenguva refu chekuchengetedza muhuwandu hwekudzikisa zvishoma nezvishoma mudumbu (sezvinoitwa mwana).

Kuchengetedza kurapa kunopa nzvimbo inogara yakasimudzwa yehafu yepamusoro yedu, kugara uchipa mwana muzvikamu zviduku zvezvokudya zvisingagumi. Mufambiro uyewo zvekare zvekudzorera uye zviratidzo zvechiratidzo.

Kukura!