Nzira yekurapa chirwere chepurocystic yepfungwa?

Iro iyo mutsara inonzi polycystic inso inoreva kuvapo kwe-cysts makuru muitsvo. Kana iwe ukasangana zvakananga nemashoko ekupedzisira, chirwere chepurocystic chirwere chirwere chinoparadzirwa pakuberekwa, ndiko kuti, congenital uye yakaratidzwa nekuvapo kwe-cyst muzvipi zviviri. Ichi ndicho chinonyanya kuratidzwa chiremerera chechimiro ichi uye hachiwanzobatanidzwa nemafanana akafanana, polycystic chiropa, uye polycystic pulmonary disease. Chirwere ichi chinobva kune chimiro chechimiro, ndiko kuti, mhuri yose inorwara, sekutonga. Kazhinji kacho kubva ku polycystosis inosangana nemafungo maviri. Nechiitiko ichi, kuumbwa kwe-cysts kunowanikwa panhandare yemutsvo wechipiri, iyo inokonzera kusakosha kwebasa rakavanzika remakona mashoma nephron particle. Ikozvino, mamiriro ezvinhu akadaro sepurocystic inyo inotungamirira ku stenosis ye renal tubules uye kuwedzera kwekumanikidzwa mavari. Ma cysts akagadzirwa ane urea, uric acid, sarti nezvimwe zvinodhaka zveropa. Iko kusvibiswa kwemakumbo emakumbo ne cysts kunotungamirira kuhosi yeropaji uye kupera kwoupenyu kwehuwandu. Uye saka, mushure mekunyora kwemashoko, tinogona kufunga nezvekurapa polycystosis yeitsvo, uyewo etiology yechirwere, kliniki uye zviratidzo zvechirwere uye, zvechokwadi, kurapwa kwepurocystic kidyo.

Pathologically, kune marudzi maviri ehosha iyi: munhu mukuru uye mwana. Polycystic inyo inogoneka neine autosomal inowanzo geni, kureva kuti, yakapfuudzwa kubva kumubereki kusvika kumwana, zvakanaka, kana nhaka nerudzi rwemotokari-gadziriro yekudzivirira, iko, kana vabereki vose vari kutakura chirwere chacho. Chirwere chePycycystic chinetso chinoitika nekuda kwekutyora kwechimiro chetsvo kana kuumbwa kwayo uye bookmarking mumazuva ekuberekwa, uye dzimwe nguva ingoerekana ichitanga nhamba shoma yemasero anoshaiwa basa repvo. Tsanga dzacho dzinogadzirwa apo paine kusakosha kusina kuenzana kwekubatana pakati peanoral tubules zvakananga ne glomeruli kana kuti iyo yakasvibiswa.

Ndezvipi zviratidzo zvinogona kugutsikana mukuvapo kwechirwere uye kubetsera kunzwisisa: nzira yekurapa polycystosis yeiyo mafungiro ezvo kana kuti chiremba chekuregererwa? Izvi zviratidzo zvakadai sekurwadziwa kwakanyanya uye kunorwadza munharaunda yegurukota, kukwirira kweropa, kuora mwoyo uye kurutsa. Aya ndiwo mazita ezviratidzo izvo murwere iye pachake angazviona, uye zviratidzo zvinowanikwa muma laboratories zvinosanganisira kuvapo kwezviratidzo zvehutachiwana muropa (leukocytosis, lymphocytosis, ESR inowedzera zvishoma) uye hematuria (ropa mumuguta) uye pyuria (pus mumuguta). Kuchikirini, muchidimbu, unogona kutaura mazwi mashomanana. Tsanangudzo yemakiriniki zviratidzo munyaya ino yakakosha zvikuru, sokuti, sezvazvakanyorwa pasi apa, kurapwa kwepurocystic itsvo zviratidzo, izvo, zvinodhaka zvinosarudzwa zvinobvisa zviratidzo zvechirwere. Uye saka, maipurocytetic inyo muvana vaduku yakaipa kwazvo, kazhinji kutarisirwa hakubatsiri, mugumisiro wechirwere ndiko kufa kwemukomana kubva kuUremia (kuzvidzora kwemuviri nekuda kwekushaya simba). Muvanhu vakuru, chirwere chinonzi polycystic chinopinda zvishoma nezvishoma uye zvakajeka chinopatsanurwa kuva matanho matatu: kubhadhara, subcompensation, decompensation. Nharaunda imwe neimwe ine zvimene zvayo. Muchikamu chekutanga chechirwere chepurocystic, iyo iri, mumutambo wekubhadhara, zviratidzo hazvisati zvaratidzwa uye, maererano naizvozvo, hapana kumhan'arira kubva kumurwere kuuya. Muchikamu chechipiri, kugadziriswa, kune kakato zviratidzo zvekushaya simba kwechirwere. Iko kunenyota kunorwadza, muromo wakaoma, kusimba kwemusoro kunowedzera, kuwedzera kweropa kunowedzera kusagadzikana. Kune pyesis ye cysts, iyo inofambidzana ne chills, fever, mukuongorora ropa nerukocytosis uye kuwedzera ESR. Matombo anokwanisa kuva muinso anogona kukonzera kukanganisa kwechirwere colic. Uye kana chirwere chacho chichienda kumutsara wechitatu, uraemia inokura. Panguva ino, chirwere chacho chinotova chiduku kudarika pane zviviri zvakapfuura. Izvi zvinotora kwemakore, izvo zvinotungamirira kukurudzirwa kwekusingaperi kwekushaya simba. Kuora kwakanyanya mumuviri wemurwere kunoitika pakarepo mushure mekubatanidzwa kwechirwere chechipiri, somuenzaniso, SARS, furuwenza nezvimwe zvakadaro. Zvinosuruvarisa, mushure mekunyatsoongorora chirwere chepurocystic yepfungwa, hupenyu hwevarwere huwandu hwemakore anopfuura gumi nemashanu.

Nezvekurapa kwetsvo dzakagadziriswa ne polycystosis, inobatwa zviratidzo, izvo, hakuna hutachiona hwakakodzera hwevose. Kana murwere asingatendi, uye pakanga pasina hosha isingakundiki, ipapo chiremba anorondedzera kudya kwakasimba kwazvo. Nokuda kwehutano hweropa kunopa zvinoderedza kuderedza ropa, kana murwere ane pyelonephritis, mishonga inorwisa mabhakitiriya nemishonga yeuroseptic inorayirwa. Kufuridzira kwe-cysts uye kuvapo kwematombo mu tubules kunogona kudii kupindira. Kana chete ma cysts asina kuwanikwa anowanika, zvino bvisai mvura yakasvibiswa nechavharo. Iyi nzira inoitwa pasi peanesthesia. Mushure mekurasikirwa kwekunzwisisika, nhovo isina kuvhara, ine tsvina inoputirwa nekurova mafungiro, uye mvura inoshandiswa inobatwa, nhoyo imwechete inotorwa kuti iongororwe. Kwete nguva dzose nzira idzi dzekurapa dzinobvisa zviratidzo zvose zvechirwere uye kuponesa kuporesa, mamiriro ehutano, kliniki yechirwere inobva kune ma cysts pachawo, hukuru hwavo, kukuvara. Iyo yakaipisisa mamiriro ezvinhu, kana ipiyo ichirasikirwa nekwakwanisa kwayo kukonzera urini, zvino chirwere chepfungwa uye hemodialysis inodiwa, iyo mune ramangwana inotungamirira kumanikidziro ekumanikidzwa kwepfungwa. Zvinosuruvarisa, nehosha iyi, kuzvirapa kunongowedzera hutano hwemurwere uye iyo yechirwere. Mune zviitiko zvose, kuputsa kwepimpumu basa rinofanira kurongedza chiremba. Nokurwadziwa munharaunda ye lumbar, hematuria uye kuvapo kwehutachiona hutachiona, haufaniri kuenda kuna chiremba zvishoma nezvishoma. Zvakanaka, sechiyero chekudzivirira, unogona kuziva kana une hama dziri mumhuri yako dzakange dziine kana dziri kurwara nechirwere chepurocystic. Mukuvapo kwechirwere chakadai, unofanirwa kuongororwa urological uye usanyora zvishoma nezvishoma. Yeuka kuti nekusaremekedzwa kana kusaremekedza kurwara, murwere ane mukana (25%) kutumira chirwere kumwana anouya.